Severe haemolysis and renal failure in a patient with paroxysmal nocturnal haemoglobinuria.
نویسندگان
چکیده
Transfusion of about 60 ml of ABO incompatible plasma in 4 units of pooled platelets precipitated severe haemolysis, unmasking the emergence of paroxysmal nocturnal haemoglobinuria (PNH), in a patient with aplastic anaemia. In vitro tests showed that her red cells were lysed by both ABO compatible and incompatible plasma from normal donors. The behaviour of this case and the in vitro results suggest that it might be hazardous to relax the longstanding recommendation on transfusing patients with PNH by restricting the washing of blood components to those containing ABO incompatible plasma.
منابع مشابه
Paroxysmal nocturnal haemoglobinuria with renal, infective and immunological abnormalities.
Introduction Paroxysmal nocturnal haemoglobinuria (PNH) is a rare disease characterized by a membrane abnormality of red cells leading to episodic haemolysis. It has only occasionally been observed in the elderly (Sirchia and Lewis, 1975). The rarity of the disease, the insidious development of symptoms and variety of presentations mean that diagnosis may be incorrect or delayed (Polli et al., ...
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عنوان ژورنال:
- Journal of clinical pathology
دوره 45 2 شماره
صفحات -
تاریخ انتشار 1992